Family screening event

Question 6: Henry is a 46-year-old man who has attended a family screening event and has been referred for a follow-up EKG. He denies seizures, dizziness, or syncope, is active and maintains a healthy BMI. He takes no daily medications. His family history is remarkable for his father who died at age 50 from a heart-related event, and his brother, who died at 3 months ago, from sudden cardiac death, which is the reason Henry decided to attend the screening event. Henry’s EKG shows a lengthened QT interval.

,1. What condition does Henry likely have?

2. What is the potentially lethal heart problem that can develop as a result of this condition? 3. What can you tell Henry about the genetics of this condition? 4. Would genetic testing be appropriate for Henry and his children? Why or why not?